[PDF] Management of surgery in children at risk of hypoglycaemia

British Inherited Metabolic Disease Group
British Inherited Metabolic Disease Group (BIMDG)
Publication date:
22 May 2013


Patients with several metabolic diseases are at risk of hypoglycaemia and other metabolic disturbances during fasting. These potentially catastrophic events can be avoided by providing adequate amounts of carbohydrate. Blood glucose should be maintained >4 mmol/l at all times.

The following instructions apply to:

  • Glycogen storage diseases: all types, although the fasting tolerance varies widely
  • Disorders of gluconeogenesis: fructose 1,6-bisphosphatase deficiency
  • Ketotic and poorly documented hypoglycaemia

Hyperinsulinism is managed by the paediatric endocrinologists.