[PDF] Ketotic hypoglycaemia

British Inherited Metabolic Disease Group
British Inherited Metabolic Disease Group (BIMDG)
Publication date:
22 May 2013


Ketotic hypoglycaemia is a poorly understood condition that most commonly affects young children between the ages of one and five years.  The history is characteristic.  A toddler who is unwell with an intercurrent infection goes to bed having had little to eat in the evening.  The next morning they are found encephalopathic or having a fit.  The child recovers quickly on being given glucose orally or intravenously.  Even if the presentation is typical, it is important to exclude other disorders

Sections of this guideline include: background, admission, initial and ongoing management, oral and intravenous feeding, progress monitoring and discharge.

Last reviewed in April 2017